Hydrometrocolpos, Symptomps and Treatment for Hydrometrocolpos
What is Hydrometrocolpos?
Hydrometrocolpos is a rare congenital anomaly and serious life threatening condition in the newborn infant due to its long-term compression sequelae and associated congenital anomalies. It is the accumulation and distention of the uterus and vagina by a fluid other than blood or pus. The spectrum of hydrometrocolpos is broad, ranging from mild cases undetected until adolescence to more severe conditions described prenatally as a large pelviabdominal cystic mass. Clinical investigation revealed hydrometrocolpos, precocious puberty, urogenital sinus and other multiple malformations.
Diagnosis of Hydrometrocolpos
Prenatal diagnosis of hydrometrocolpos by sonogram allows appropriate management during the prenatal and neonatal period. The combination of hydrometrocolpos and polydactyly is the cardinal hallmark feature of McKusick-Kaufman Syndrome.
The most importent treatment Hydrometrocolpos :
- The baby showed masculinisation without clitoral enlargement and a narrow urogenital sinus with resulting hydrometrocolpos.
- Surgical hydrometrocolpos for imperforate should require only one definitive procedure to evacuate retained secretions and to assure maintenance of patency.
- Postoperative follow-up is deferred for 6-8 weeks to allow the patient to reestablish a menstrual cycle
- It is possible that dexamethasone treatment which is initially inadequate increases the risk of this latter complication.